DYSPNEA IN AN ADULT WITH ATRIAL SEPTAL DEFECT AND SJÔGREN’S SYNDROME: WHO’S TO BLAME?

ASD and more frequently the ostium secundum type is a relatively common adult congenital heart disease. Sjogren’s syndrome on other side second most frequent auto immune disease, Involving lungs in 9–20% of patients. We report case 69 years old woman, complaining long-standing dyspnea was diagnosed with syndrom. Her CT scan pulmonary function tests were normal. That lead to investigate for hypertension as potential cause her dyspnea. A TTE performed estimated systolic pressure at 30 mmhg, showed an OS left right shunt. Right catheterization calculated mPaP 20 mmhg. She scheduled percutaneous closure ASD. There are only few cases reporting association between polyendocrine syndrome, even fewer without syndrome. Farook Al. discussed women presenting SS complicated PAH, suggesting two pathologies by inflammatory process, Inoue et presented polyartritis rheumatoid inducing shunt through patent foramen oval. In our case, mild probably reason dyspnea, there no interstitial lung disease normal PFT.Unfortunately, sufficient data eventual The learning point importance screening unexplained